該基因編碼一種線粒體蛋白，該蛋白是琥珀酸脫氫酶復合物活性所需的一個亞單位的黃素化所必需的。該基因突變與副神經節瘤相關。[由RefSeq提供，2010年7月]
This gene encodes a mitochondrial protein needed for the flavination of a succinate dehydrogenase complex subunit required for activity of the complex. Mutations in this gene are associated with paraganglioma.[provided by RefSeq, Jul 2010]